Rectal Involvement of Klippel-Trenaunay Syndrome. |
Cheon, Seong Hui , Lee, Suk Hwan , Park, Eung Bum |
1Department of Surgery, Ewha Womans University College of Medicine, Seoul, Korea. 2Department of Surgery, Kyunghee University College of Medicine, Seoul, Korea. leeshdr@khu.ac.kr |
|
|
|
Abstract |
Klippel-Trenaunay syndrome (KTS) is a rare congenital disorder and is essentially a disorder of capillary, venous, and lymphatic malformations. Hematochezia is the most common symptom associated with intestinal hemangiomatosis and remains one of the life-threatening emergencies in KTS. We reported one patient of KTS presented with rectal bleeding and severe anemia who was successfully managed by sphincter-saving operation. |
Key Words:
Rectal bleeding; Klippel-Trenaunay syndrome; Coloanal anastomosis |
|